Foix-Alajouanine syndrome mimicking a spinal cord tumor

Síndrome de Foix-Alajouanine simulando um tumor intramedular espinal

Renan Salomão Nathalie Henriques Silva Canêdo Guilherme P. Abrão Carlos Lima Marcus André Acioly About the authors

Summary

Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor.

Keywords:
dural arteriovenous fistula; Foix-Alajouanine syndrome; spinal cord glioma; subacute necrotizing myelopathy

Associação Médica Brasileira R. São Carlos do Pinhal, 324, 01333-903 São Paulo SP - Brazil, Tel: +55 11 3178-6800, Fax: +55 11 3178-6816 - São Paulo - SP - Brazil
E-mail: ramb@amb.org.br