Diverticulitis in adolescent with Williams Syndrome: case report

The Syndrome of Williams is a rare genetic illness, attributed the deletion of the gene of the elastin in chromosome 7. It is characterized by aortic stenosis, bladder diverticula's, constipation, light mental retardation, dysmorphic facies, weakness of the wall of the bladder and colon that they lead to the sprouting of diverticula. A case of acute diverticulitis in patient of 18 years is told, the result of the clinical treatment during 5 years and the differential diagnosis of acute abdomen in this illness. The indication of elective colectomy is argued, considering the unfamiliarity of the natural history of the diverticulitis in the syndrome.

Diverticulitis; acute abdomen; adolescent; Williams Syndrome


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