Abstract
Clinical data:
Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation.
Chest radiography:
Demonstrates cardiomegaly and prominent pulmonary vascular markings.
Electrocardiography:
Shows right ventricular hypertrophy and left anterior fascicular block.
Echocardiography:
Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein.
Computed tomography angiography:
This complementary imaging exam was performed to confirm the diagnosis.
Diagnosis:
The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated.
Operation:
The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.
Keywords:
Heart Septal Defects; Atrioventricular Septal Defect; Pulmonary Veins; Cardiopulmonary Bypass
