A 6-year-old female child sought medical service due to a gastrointestinal malformation. During a medical follow-up a partial absence of the inferior vena cava was diagnosed, which is a rare congenital alteration, involving the vascular drainage from the inferior segment of the body. Imaging exams were performed, which contributed to evaluation and description of the case. Conservative treatment with an oral anticoagulant was maintained. The patient presents good evolution after a long-term cardiovascular follow-up.
Venae cavae; Vena cava, inferior; Heart Defects, congenital