Juvenile Xanthogranuloma is a benign disease, classified as Class II histiocytosis, generally characterised by cutaneous nodules, most commonly, in the head and neck region. It often occurs in childhood and it is rare in adults. Extracutaneous lesions are uncommon, and the most common extracutaneous lesion is in the eye. We report a case of juvenile xanthogranuloma occuring in the nasal cavity, which is extremely rare in literature. We found only one report of xanthogranuloma in nasal cavity in the English Literature¹. Case report: D.C.S., female, 12 years-old was referred with a history of progressive right sided nasal obstruction for 18 months. In another hospital, she had had diagnostic of Rhinoscleroma. The clinical examination revealed a solid lesion in the right nasal cavity with an increased dorsal nose and deslocation of right eye. The solid lesion was excised by Degloving technique. The histopathological and immunohistochemical diagnosis was of juvenile xanthogranuloma. Juvenile Xanthogranuloma is a benign disease which regresses spontaneously. We observed the patient with nasofibroscopy for five months after surgery. Until today, she is asymptomatic and without recurrence.
juveline xanthogranuloma; nasal cavity; tumor; immunohistochemic; histiocytosis