SciELO - Scientific Electronic Library Online

vol.25 issue4Evaluation of reading performance in students from 3rd to 7th grade levels, with different text typesManagement of dysphagia in Parkinson's disease and amyotrophic lateral sclerosis author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Services on Demand




Related links



On-line version ISSN 2317-1782


ZEIGELBOIM, Bianca Simone et al. Audiological evaluation in spinocerebellar ataxia. CoDAS [online]. 2013, vol.25, n.4, pp.351-357.  Epub Aug 16, 2013. ISSN 2317-1782.

PURPOSE: To describe the audiological and electrophysiological results in patients with spinocerebellar ataxia (SCA). METHODS: Retrospective and cross-sectional studies were performed. Forty-three patients were assessed using the following procedures: anamnesis and otolaryngologic exam, pure tone audiometry, acoustic immittance measures and brainstem auditory evoked potential (BAEP). RESULTS: Patients showed gait abnormality (83.7%), speech disorder (48.8%), dizziness (41.8%) and dysphagia (39.5%). Hearing loss was referred in 27.9% of the cases; in the audiometric exams, 14 patients (32.5%) presented disorders; in SCA 3, 33.3%; in SCA 2, 12.5%; in SCA 4, 100.0%; in SCA 6, 100.0%; in SCA 7, 100.0%; in SCA 10, 50.0%; and in undetermined SCA, 21.4%. In BAEP, 20 patients (46.5%) were abnormal, being 58.3% in SCA 3, 62.5% in SCA 2, 100.0% in SCA 6, 100.0% in SCA 7, 66.7% in SCA 10 and 14.2% in undetermined SCA. While in acoustic immittance, 19 patients (44.1%) presented disorders, being 50.0% in SCA 3, 50.0% in SCA 2, 100.0% in SCA 4, 100.0% in SCA 6, 100.0% in SCA 7, 33.3% in SCA 10 and 28.5% in undetermined SCA. CONCLUSION: The most evident abnormalities in the audiological evaluation were the predominance of the down-sloping audiometric configuration beginning at 4 kHz bilaterally and the bilateral absence of acoustic reflex at the frequencies of 3 and 4 kHz. In the electrophysiological evaluation, 50% of the patients showed abnormalities with prevalence of an increase of the latency of waves I, II and V and of the interval in the interpeaks I-III, I-V and III-V.

Keywords : Spinocerebellar degenerations; Spinocerebellar ataxias; Ataxia; Hearing; Hearing disorders; Audiometry, evoked response; Audiometry; Evoked potentials, auditory.

        · abstract in Portuguese     · text in Portuguese     · English ( pdf ) | Portuguese ( pdf )


Creative Commons License All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License