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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.33 no.2 São Paulo June 1975 

Miopatia ocular descendente


Descending ocular myopathy: a case report



Marcos R. G. de FreitasI; Osvaldo J. M. NascimentoII

IResponsável pela Disciplina de Neurologia junto à Chefia do Departamento de Medicina Clínica da Universidade Federal Fluminense, Auxiliar de Ensino de Neurologia da UFRJ (Instituto de Neurologia Deolindo Couto), Serviço do Prof. Bernardo Couto
IIAuxiliar de Ensino da Disciplina de Neurologia da Universidade Federal Fluminense, Bolsista do Conselho de Pesquisas da UFRJ no Instituto de Neurologia Deolindo Couto (Serviço de Neuropatologia do Prof. Alexandre Alencar)




Os autores apresentam caso de paciente jovem, do sexo feminino, com afecção muscular primária ocular e faríngea sem caráter familial. Foram feitos estudos eletromiográficos e histopatológicos musculares que confirmam o caráter miogênico do processo. É feita comparação entre a miopatia ocular e a miopatia ocular descendente, acreditando os autores que seriam variantes


The case of a 23 years old female patient, with primary involvement of the extraocular and faringeal muscles without familiar history is reported. Electromyographic and muscular biopsy studies proved the myogenic nature of the process. A clinical comparison between the ocular myopathy and the descending ocular myopathy is made, the authors thinking that both of them would be variants of the same muscle disease.



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