Resumos
Os autores apresentam caso de paciente jovem, do sexo feminino, com afecção muscular primária ocular e faríngea sem caráter familial. Foram feitos estudos eletromiográficos e histopatológicos musculares que confirmam o caráter miogênico do processo. É feita comparação entre a miopatia ocular e a miopatia ocular descendente, acreditando os autores que seriam variantes
The case of a 23 years old female patient, with primary involvement of the extraocular and faringeal muscles without familiar history is reported. Electromyographic and muscular biopsy studies proved the myogenic nature of the process. A clinical comparison between the ocular myopathy and the descending ocular myopathy is made, the authors thinking that both of them would be variants of the same muscle disease.
Miopatia ocular descendente
Descending ocular myopathy: a case report
Marcos R. G. de FreitasI; Osvaldo J. M. NascimentoII
IResponsável pela Disciplina de Neurologia junto à Chefia do Departamento de Medicina Clínica da Universidade Federal Fluminense, Auxiliar de Ensino de Neurologia da UFRJ (Instituto de Neurologia Deolindo Couto), Serviço do Prof. Bernardo Couto
IIAuxiliar de Ensino da Disciplina de Neurologia da Universidade Federal Fluminense, Bolsista do Conselho de Pesquisas da UFRJ no Instituto de Neurologia Deolindo Couto (Serviço de Neuropatologia do Prof. Alexandre Alencar)
RESUMO
Os autores apresentam caso de paciente jovem, do sexo feminino, com afecção muscular primária ocular e faríngea sem caráter familial. Foram feitos estudos eletromiográficos e histopatológicos musculares que confirmam o caráter miogênico do processo. É feita comparação entre a miopatia ocular e a miopatia ocular descendente, acreditando os autores que seriam variantes
SUMMARY
The case of a 23 years old female patient, with primary involvement of the extraocular and faringeal muscles without familiar history is reported. Electromyographic and muscular biopsy studies proved the myogenic nature of the process. A clinical comparison between the ocular myopathy and the descending ocular myopathy is made, the authors thinking that both of them would be variants of the same muscle disease.
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Datas de Publicação
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Publicação nesta coleção
09 Abr 2013 -
Data do Fascículo
Jun 1975