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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.49 no.4 São Paulo Dec. 1991

http://dx.doi.org/10.1590/S0004-282X1991000400018 

CONTENTS CONTEÚDO

 

Hemorragia maciça intratumoral em esclerose tuberosa estudo autóptico de um caso

 

Massive intratumoral hemorrhage in tuberous sclerosis: autopsy study of a case

 

 

Lígia M. Barbosa-CoutinhoI; Eduardo Lahude LimaII; Ricardo Olaechea GadretIII; Nelson Pires FerreiraIV

IProfessora Adjunta do DP - Trabalho realizado no Departamento de Patologia (DP) da Fundação Faculdade Federal de Ciências Médicas de Porto Alegre (FFFCMPA)
IIMédico Residente do DP - Trabalho realizado no Departamento de Patologia (DP) da Fundação Faculdade Federal de Ciências Médicas de Porto Alegre (FFFCMPA)
IIIDoutorando da FFFCMPA - Trabalho realizado no Departamento de Patologia (DP) da Fundação Faculdade Federal de Ciências Médicas de Porto Alegre (FFFCMPA)
IVProfessor Adjunto de Neurocirurgia da FFFCMPA - Trabalho realizado no Departamento de Patologia (DP) da Fundação Faculdade Federal de Ciências Médicas de Porto Alegre (FFFCMPA)

 

 


RESUMO

O caso de um menino com esclerose tuberosa, apresentando o quadro clínico típico e que morreu com hemorragia intratumoral maciça, é estudado. A autópsia parcial de crânio revelou hemorragia cerebral maciça à esquerda, no interior da qual se identificou um tumor que, à microscopia, mostrou se tratar de astrocitoma subependimário de células gigantes. Este é o segundo caso, na literatura, no qual um paciente com esclerose tuberosa morre de hemorragia maciça intratumoral, com inundação ventricular.


SUMMARY

A case of a 13-years-old boy with tuberous sclerosis manifested with the complete syndrome that died with a massive intratumoral hemorrhage is presented. The post mortem examination of the brain disclosed a massive left parenchymatous brain, hemorrhage with intraventricular component. In the hemorrhage, near the lateral ventricle wall, a subependymal giant cell astrocytoma was found. This is the second case in the literature of tuberous sclerosis which cause of death was an intratumoral massive hemorrhage.


 

 

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

 

 

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