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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.52 no.1 São Paulo Mar. 1994

http://dx.doi.org/10.1590/S0004-282X1994000100019 

Syndrome of continuous muscle fiber activity: case report with 11-year follow-up

 

Síndrome de atividade contínua da fibra muscular: relato de caso com seguimento de 11 anos

 

 

José Teotônio de OliveiraI; Igor Levy-ReisII

INeurology Service, Hospital of Clinics, Federal University of Minas Gerais, Medical School, Belo Horizonte: Assistant Professor
IINeurology Service, Hospital of Clinics, Federal University of Minas Gerais, Medical School, Belo Horizonte: Resident. Presented at the 15th Brazilian Congress of Neurology (Porto Alegre, October 1992)

 

 


SUMMARY

A 16-year-old male patient who presented with muscle stiffness and dysphonia is described. Electromyography revealed continuous motor activity that was unaffected by peripheral nerve block or general anaesthesia, but was abolished by curare. The patient had a marked improvement after using phenytoin. The follow-up 11-years later corroborates with the proposed benignity of this syndrome, in spite of being dependent on medication.

Key words: muscle stiffness, continuous muscle fiber activity, Isaacs' syndrome.


RESUMO

É relatado o caso de um paciente de 16 anos de idade do sexo masculino com quadro de rigidez muscular e disfonia. Eletromiografia revelou atividade motora contínua que não era alterada por bloqueio do nervo periférico ou anestesia geral, mas era abolida por curare. O paciente apresentou acentuada melhora após o uso de fenitoína. O seguimento do caso 11 anos mais tarde vem corroborar o proposto caráter benigno desta síndrome, apesar de o paciente ainda depender da medicação.

Palavras-chave: rigidez muscular, atividade de fibra muscular contínua, síndrome de Isaacs.


 

 

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

 

 

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Aceite: 22-setembro-1993.

 

 

Dr. José Teotônio de Oliveira - Serviço de Neurologia, Hospital das Clínicas UFMG - Av. Alfredo Balena 190 -30130-100 Belo Horizonte MG - Brasil.

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