An unusual case of Paget's disease of bone, presenting as a maxillary disease, is discussed. This rare manifestation of a systemic disease led to an initial difficulty in establishing the diagnosis; indeed, the etiology was only determined after the lesion biopsy. Bisphosphonates were used with a good response. We highlight in this article the need for a multidiscipli-nary follow-up of such patients due to odonthological complications of the disease when localized in the jaw.
Osteitis deformans; Paget's disease; Bisphosphonates; Bone remodeling