Resumos
São descritos dois casos de pacientes com anemia falciforme (AF) que desenvolveram complicações neurológicas. Os estudos angiográficos mostraram alterações semelhantes àquelas encontradas na doença moyamoya. Estes achados ocorrem também em outras patologias e são resultado de mecanismo de compensação a oclusão das artérias da base do cérebro. São comentados os riscos e as precauções para a realização da angiografia cerebral.
Two cases of sickle cell disease with neurological complications are described. Cerebral angiograms were performed and a characteristic moyamoya-like angiographic pattern was demonstrated. This pattern results from a compensatory vascularization which may follow occlusion of the arteries at the base of the brain in several diseases. The risks of angiography and appropriate precautions are emphasized.
CONTENTS CONTEÚDO
J. O. Alarcon-AdornoI; Adelmo FerreiraII; M. MuszkatIII
IDoutor em Neurocirurgia pela Escola, Paulista de Medicina (EPM), Neurocirurgião do HIMJ - Hospital Infantil Menino Jesus (HIMJ), São Paulo
IIPós-graduando em Neurocirurgia da EPM, Neurocirurgião do Hospital Municipal A.R. Saboya - Hospital Infantil Menino Jesus (HIMJ), São Paulo
IIIMédico do HIMJ - Hospital Infantil Menino Jesus (HIMJ), São Paulo
RESUMO
São descritos dois casos de pacientes com anemia falciforme (AF) que desenvolveram complicações neurológicas. Os estudos angiográficos mostraram alterações semelhantes àquelas encontradas na doença moyamoya. Estes achados ocorrem também em outras patologias e são resultado de mecanismo de compensação a oclusão das artérias da base do cérebro. São comentados os riscos e as precauções para a realização da angiografia cerebral.
SUMMARY
Two cases of sickle cell disease with neurological complications are described. Cerebral angiograms were performed and a characteristic moyamoya-like angiographic pattern was demonstrated. This pattern results from a compensatory vascularization which may follow occlusion of the arteries at the base of the brain in several diseases. The risks of angiography and appropriate precautions are emphasized.
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Dr. Juana Oscar Alarcón Adorno - Rua Coronel Lisboa 454 - 04020 São Paulo SP - Brasil.
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Anemia falciforme alterações angiográficas cerebrais
Datas de Publicação
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Publicação nesta coleção
22 Fev 2011 -
Data do Fascículo
Mar 1991