Ménétrièr disease in a pediatric patient with particular reference to echoendoscopy, endoscopic and anatomopathological presentation and evolutionary and therapeutic aspects

Doença de Ménétrier em paciente pediátrico com destaque para apresentação eco e endoscópica, anatomopatológica e aspectos evolutivos e de conduta

Vinicius S. Garcia Monica Maria D. Alvares Cabral Simone D. Carvalho Vitor N. Arantes About the authors


Ménétrier's disease (MD) is included in the group of hypertrophic gastropathy; is a rare gastric hyperplasia that affects adults and children, with different behavior between these groups. We know that its etiology is related to allergens and co-infections. It's characterized by the hypertrophy of the gastric folds, with the appearance of cerebral convolutions on Upper Gastrointestinal Endoscopy (UGE) and, histologically, by the mucosal hypertrophy at the expense of foveolar hyperplasia and atrophy of the glands in body and fundus of the stomach. The UGE together with the gastric tissue biopsy confirms the diagnosis. What concerns us in the following case, however, is patient's long-lasting evolution, about eight years.

Key words:
pediatrics; gastropathy; endoscopy of the gastrointestinal tract; gastroenterology; histology

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