Monoscleral fixation of IOL after extracapsular extraction of subluxated lenses in patients with Marfan syndrome

Fixação monoescleral da LIO após extração extracapsular de cristalinos subluxados em pacientes com síndrome de Marfan

PURPOSE: To describe a technique of monoscleral fixation of the intraocular lens (IOL) after extracapsular extraction of subluxated lens in patients with Marfan syndrome. Design: Noncomparative, interventional case series. METHODS: A retrospective study was conducted on 14 eyes of 7 consecutive patients with subluxated lens associated with Marfan syndrome. Surgery was indicated when: 1) a lens border was observed in the pupil area with the pupil under normal lighting causing glare; or 2) the best corrected visual acuity was less than 20/70; or 3) the patient complained of monocular diplopia. Patients with a history of glaucoma, retinal detachment, trauma or other systemic diseases were excluded. RESULTS: The mean postoperative follow-up was 15.43 ± 9.33 months (range, 6 to 30 months). The best spectacle-corrected visual acuity varied from 20/25 to 20/60, where 71.43% reached 20/30 or better. No case showed a worsening of visual acuity, nor were there any intraoperative or postoperative complications (intraocular lens decentration, pupilar block, glaucoma or retinal detachment). The most frequent postoperative complication was astigmatism, observed in 3 eyes (21.43%) presenting values greater than 1.5 D. CONCLUSIONS: This technique showed very good surgical and visual results and few complications, providing a surgical option for cases of ectopia lentis associated with Marfan syndrome, especially in some countries or regions where phacoemulsification is not available.

Marfan syndrome; Ectopia lentis; Cataract extraction; Ophthalmologic surgical procedures; Intraocular lens implantation

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